Neurofibromatosis and small bowel adenocarcinoma: an unrecognised association.
نویسندگان
چکیده
We present a review of the reported cases and describe a fifth of neurofibromatosis with small bowel adenocarcinoma and concurrent leiomyomas, indicating a previously unrecognised association.
منابع مشابه
Intestinal neurofibromatosis and small-bowel adenocarcinoma: a single case study.
OBJECTIVE Patients with Von Recklinghausen's disease (neurofibromatosis type 1) are at increased risk of developing various tumours. However, the coexistence of neurofibromatosis with small-bowel adenocarcinoma is exceedingly rare. We present an uncommon case of neurofibromatosis type 1, involving the small bowel in a 73-year-old man, who was admitted to our department with signs of acute abdom...
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CONTEXT Gastrointestinal (GI) involvement is present in about one quarter of cases of neurofibromatosis type 1 (NF1). Adenocarcinomas have been reported in several organs. Gastrointestinal stromal tumors are the most common GI lesion seen in NFI. GISTs in combination with ampullary neuroendocrine tumors in NF-1 have been reported rarely. CASE REPORT We present the case of a 44-year-old man wh...
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Malignant tumors of the small bowel are rare and little is known about their etiology, although adenocarcinomas share certain epidemiological features with colorectal cancer. This study investigated what cancers, if any, occurred as second neoplasms following adenocarcinomas, malignant carcinoid tumors, lymphomas, and sarcomas of the small bowel. For all 2581 cases of small bowel malignancy reg...
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BACKGROUND Although Crohn's disease (CD) is thought to predispose to adenocarcinomas of the small bowel, the association has not been well studied in an older population. AIMS The objective of our study was to evaluate the association of CD with small bowel cancer in a population-based case-control study. METHODS All cases of small bowel cancer in persons 67 and older in the Surveillance, E...
متن کاملPrimary adenocarcinoma of the duodenum associated with cutaneous neurofibromatosis (von Recklinghausen's disease).
Introduction The association of neurofibromatosis with malignant tumours of the neural crest is well documented. Neurofibromatosis may also be associated with other malignant tumours such as carcinoid of the ampulla of Vater (Barber, 1976), adenocarcinoma of the pancreas (Kellar and Logan, 1977), adenocarcinoma of the colon (Jenkins and Gill, 1972), Wilms' tumour (Stay and Vauter, 1977), rhabdo...
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ورودعنوان ژورنال:
- Gut
دوره 28 9 شماره
صفحات -
تاریخ انتشار 1987